平滑肌肉瘤在儿童极为罕见 ,尤其是发生在软组织。作者报道了 16岁以下的儿童患者 2 0例。主要发病部位是躯干、下肢和颈部 ,亦可发生在上肢、肩、舌和纵隔。大多数位于深部软组织 ,无一例发生在皮肤。术前病变持续时间从几天到 1年 ,多数为无痛性包块。病理表现 :肿瘤直径 0 Leiomyosarcoma is extremely rare in children, especially in soft tissue. The authors reported 20 children under 16 years of age. The main site of disease is the trunk, lower extremities and neck, can also occur in the upper limbs, shoulders, tongue and mediastinum. Most are located in deep soft tissue, none of which occurs on the skin. Preoperative lesion duration from a few days to 1 year, the majority of painless mass. Pathological findings: tumor diameter 0