血友病类出血性疾病包括血友病甲(血友病A、AHG缺乏症、因子Ⅷ缺乏症),血友病乙(血友病B,PTC缺乏症,因子Ⅸ缺乏症),血友病丙(血友病C,PTA缺乏症,因子Ⅺ缺乏症)。是一组遗传性凝血功能障碍的出血性疾病。我们从1982年9月至1983年12月,经改良凝血活酶生成试验(改良Biggs法TGT)反其有关纠正试验确诊的血友病共13例,现分析报告如下。临床资料 13例中,血友病甲7例,血友病乙6例,未发现血友病丙。男性10例,女性3例,均为血友病乙.年龄最大者48岁,最小者28天,20岁以下8例,占61.5％,20岁以上5例,占38.4％.有家族史者3例。1女性病例父母为近亲姨表婚配。临床表现:肌肉 Hemophilia hemorrhagic diseases include hemophilia A (hemophilia A, AHG deficiency, factor Ⅷ deficiency), hemophilia B (hemophilia B, PTC deficiency, factor IX deficiency), hemophilia Disease C (hemophilia C, PTA deficiency, factor Ⅺ deficiency). Is a group of hereditary coagulation disorders bleeding disease. We from September 1982 to December 1983, the modified thromboplastin test (modified Biggs method TGT) against the correct test hemophilia a total of 13 cases, the analysis is as follows. Thirteen cases of clinical data, hemophilia A 7 cases, hemophilia B 6 cases, no hemophilia C was found. 10 males and 3 females, all of whom were hemophilia B. The oldest was 48 years old, the youngest was 28 days, and 8 cases were below 20 years old, accounting for 61.5%, 5 cases were over 20 years old, accounting for 38.4% 3 cases. 1 female parents of the case of close relatives aunt marriage table. Clinical manifestations: Muscle