嗜酸性淋巴肉芽肿合并肾病综合征,国内少见,本院收治1例,报告如下。 患者 男性,43岁。间断颌下淋巴结肿大2年,周身浮肿伴尿少4个月入院。2年前无明显诱因出现颌下淋巴结肿大,单发,约3×3cm,淋巴结活检病理诊断“嗜伊红淋巴肉芽肿”。数月后颌下淋巴又出现,再次手术活检同上,经强的松15mg/d及放疗后,病情稳定。停用激素后5个月(入院前4个月)无明显诱因周身浮肿、尿少,颌下淋巴结再次肿大,3～4个,尿常规蛋白(+++),尿蛋白定量21g/24h,服强的松60mg/d,静注环磷酰胺8g后肿大淋巴结消失,尿蛋白减至7g/24h,转我院。既往无肾炎肝炎史。入院体检:体温36℃,脉搏80次,血压18/11kPa。满月脸,面 Acidophilic lymphogranulomatous nephrotic syndrome, rare in our hospital admitted to a case, the report is as follows. Male patient, 43 years old. Intermittent submandibular lymph nodes 2 years, whole body edema with urine less 4 months hospitalization. 2 years ago, no obvious incentive submandibular lymph nodes, solitary, about 3 × 3cm, lymph node biopsy pathological diagnosis of “eosinophilic granuloma.” After a few months submandibular lymph appears again biopsies again Ibid by prednisone 15mg / d and radiotherapy, the disease was stable. There were no obvious causes of edema, oliguria, submandibular lymph nodes enlargement in 3 to 4 months, urinary protein (+++) and urinary protein in 21 g / 24 h after 5 months of withdrawal of hormone (4 months before admission) , Prednisone 60mg / d, intravenous cyclophosphamide 8g swollen lymph nodes disappeared, urinary protein reduced to 7g / 24h, transferred to our hospital. No past history of nephritis and hepatitis. Admission medical examination: body temperature 36 ℃, pulse 80 times, blood pressure 18 / 11kPa. Full moon face, face