本文分析了2例新发病及4例以前报导过且已经证实为动脉阻塞性视网膜病脑病综合征患者。6例均为女性,年龄为21—40岁。此病的临床特征包括多发视网膜动脉分支阻塞和脑病早期主要表现行为和记忆紊乱,常有听力丧失,除脑脊汝淋巴细胞和蛋白增高外,实验室检查和X 线拍片很少出现异常。此病对皮质类甾醇类药物敏感。该综合征与 This article analyzes two new cases and four previously reported cases of arteriosclerotic retinal encephalopathy syndrome. 6 cases were female, aged 21-40 years old. The clinical features of this disease include multiple retinal artery occlusion and early manifestations of encephalopathy and memory disorders, often hearing loss, in addition to cerebrospinal fluid and lymphocytes and protein increased, laboratory tests and X-ray film rarely appear abnormal. The disease is corticosteroid sensitive. The syndrome and