小儿先天性肛门直肠畸形约有20%到30%合伴有脊髓栓系,这主要是早期胚胎发育过程中尾端神经的发育不良所致,脊髓栓系的发生率与肛门直肠畸形的严重程度密切相关。所有肛门直肠畸形患儿均应常规MRI筛查,了解是否同时存在脊髓栓系。对于存在神经功能障碍的患儿应行脊髓栓系松解手术,但对无症状患儿是否需要进行预防性手术尚存在争议。 Pediatric congenital anorectal malformations about 20% to 30% associated with tethered cord, which is mainly caused by early embryonic development of caudal nerve dysplasia, the incidence of tethered cord and the severity of anorectal malformations close Related. All children with anorectal malformation should be routine MRI screening to understand whether there are simultaneous tethered cord. For children with neurological dysfunction should be tethered spinal cord surgery, but asymptomatic children need preventive surgery is still controversial.