论文部分内容阅读
本组报告了两例胚胎性横纹肌肉瘤,一例在椎管内伴有右侧第六肋病理性骨折及胸腔包块,另一例在颅内左侧桥小脑角及左颈后皮下斜方肌上缘处,且有经枕大孔向颅内生长之趋势.手术全切肿瘤后均经病理证实.其发病特点:病程短,发展快,复发率高,病情呈进行性发展,预后极差.由于在颅内及椎管内的原发性肿瘤非常少见,两例患者均有两处病灶,其椎管内肿瘤伴有胸腔内包块者对其包块高度怀疑,但未作活检;而颅内左侧桥小脑角肿瘤患者的左颈后皮下包块则均经手术证实为胚胎性横纹肌肉瘤,究竟彼此间有无联系尚不能肯定.对其发病后术中所见,病理特点及其组织起源均作了详细介绍,此病患者全身呈恶病质,营养状况不佳,往往容易与神经系统的其它疾病相混淆.
The group reported two cases of embryonal rhabdomyosarcoma, one case of spinal canal with the sixth right rib pathological fracture and thoracic mass, the other in the left cranial left cerebellopontine angle and the left posterior subcutaneous trapezius Edge, and there is a large hole to the intracranial growth of the trend of the whole operation of the tumor were confirmed by pathology. The incidence of its characteristics: short duration, rapid development, high recurrence rate, progressive progression of the disease, the prognosis is extremely poor. Due to the rare intracranial and intraspinal primary tumors, both patients have two lesions, the intracavitary tumor associated with intrathoracic masses are highly suspicious of its mass without biopsy; and cranial The left subclavian cerebellar angle tumor in patients with left and right posterior subcutaneous mass were confirmed by surgery for embryonal rhabdomyosarcoma, whether or not the relationship between each other is still not sure.After the onset of surgery, the pathological features and tissue The origin has been described in detail, the patient’s body was cachexia, poor nutritional status, often easily confused with other diseases of the nervous system.