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神经纤维瘤病(Neurofibromasis)又称为VonRecklin ghausen氏病。典型病例国内报道较少,现将我院迂到的两例报告于下: 例1,韩×x,女,37岁,于1981年5月入院。患者自幼右眼向前凸出,随年龄之增长而加重,伴视物模糊。8年前感双上肢麻木无力,不久即出现腰部不适、双下肢麻木并软弱无力。劳动后加重,休息时稍轻。以后上述症状加重,小便频数失控,大便秘结。双下肢变细屈曲强直,间有不自主的伸屈运动。婚后未育,其母有类似疾病史。查体:胸、腹及四肢均散布着大小不等、边界清楚、棕褐色的斑,直径约1.5cm的有13处,以胸部为多。双腋窝部有对称性密集褐色小斑点。胸腹部皮肤有大小不一的结节,质地较软,粉红色,大者有短蒂。右膝盖部有直径1cm的固定结节,囊性感,触之有条索状物轻触痛。右眼球凸出约0.5～
Neurofibromasis is also known as VonRecklin ghausen’s disease. Typical cases of domestic reports less, now our hospital report of the two cases reported: Example 1, Han × x, female, 37 years old, was admitted to hospital in May 1981. The patient protruded forward with his right eye, increased with age, accompanied by blurred vision. 8 years ago, feeling upper limb numbness weakness, and soon there waist discomfort, numbness and weakness of both lower extremities. Increase after work, rest a bit lighter. After the above symptoms, urination frequency out of control, constipation. Double lower extremity flexion and stiffness, involuntary flexion and extension between the movement. Not married after marriage, the mother has a history of similar diseases. Physical examination: Chest, abdomen and limbs are scattered with different sizes, clear boundaries, brown spots, a diameter of about 1.5cm 13, to the chest as much. Double armpit Department has a symmetrical dense brown small spots. Chest and abdomen skin nodules of different sizes, texture is soft, pink, big short pedicle. The right knee has a fixed diameter of 1cm nodules, cystic sexy touch with a bar-like light touch the pain. Right eye bulge about 0.5 ~