着色性干皮病属于一种常染色体异常性遗传疾病。主要以日光照射暴露的皮肤干燥、全身皮肤雀斑样色素沉着、伴发恶性肿瘤为其临床特征。本病极为少见,而伴发两种恶性肿瘤则更为罕见。现就我科所遇到的一例报告如下: 患者:王某某,女,34岁,因患左眶下区肿物一年余,于1981年7月3日来我院就诊。患者出生后三个月即被发现全身皮肤出现紫色小点,三 Shade dry skin disease is an autosomal abnormal genetic disease. Mainly exposed to sun exposure dry skin, skin freckle-like pigmentation, with malignant tumor as its clinical features. The disease is extremely rare, but with two malignant tumors are even more rare. Now we encounter a case report is as follows: Patients: Wang Moumou, female, 34 years old, suffering from left and infraorbital tumor more than a year, in July 3, 1981 to our hospital. Three months after the birth of the patient was found purple spots on the whole body skin, three