幕上原始神经外胚层肿瘤(supratentorial primitiveneuroecdermal tumor,SPNET)十分少见,并侵犯颅骨者更为罕见,现有一例报告如下。男性,2岁半,左颞顶部包块逐渐增大20d余入院。查体:头围大,左眼睑肿胀,左眼球略外突,左颞顶区有一约8.0cm×10.0cm头皮下包块,质韧,局部头皮静脉 Supratentorial primitive neuroecrmal tumor (supratentorial primitive neuroecrmal tumor, SPNET) is very rare, and violations of the skull were more common, the current one is reported as follows. Male, 2 years and a half, the left temporal top of the mass gradually increased more than 20d admission. Physical examination: head circumference, swelling of the left eyelid, left eye slightly protruding, the left temporal top area has about 8.0cm × 10.0cm scalp mass, quality and toughness, local scalp vein