烟雾病又叫Moyamoya病,是以脑底动脉环及其附近分支狭窄或者闭塞,伴有异常毛细血管网形成为特征的脑血管疾病。脑血管造影时,脑底异常毛细血管形如吸烟时喷出的烟雾因而得名。本病1961年首先出现于日本文献,1968年Kudo对本病作了系统的描述,1977～1979年国内先后报告38例,我院自1966年以来共见到本病10例,报告如下。 Moyamoya disease, also called Moyamoya disease, is a cerebrovascular disease characterized by a narrow or occluded branch of the cerebral artery and its nearby branches with abnormal capillary network formation. Cerebral angiography, abnormal brain capillary-shaped smoke as the smoke emitted so named. The disease first appeared in Japanese literature in 1961, Kudo made a systematic description of the disease in 1968. From 1977 to 1979, 38 cases were reported in our country and 10 cases were reported in our hospital since 1966. The report is as follows.