本文报告1例原发性肝平滑肌肉瘤,并复习有关文献,对临床、病理特征作了简单介绍。肝脏原发性恶性肿瘤中癌瘤多见。肉瘤较少,仅占肝恶性肿瘤的1—2%。其中平滑肌肉瘤更为罕见,据目前国际文献仅有10余例个案报告。未见国内报告。我院遇见1例,报告如下。 This article reports a case of primary liver leiomyosarcoma, and review the literature, a brief introduction to the clinical and pathological features. In liver primary malignant tumors, cancers are more common. Less sarcomas only account for 1-2% of liver malignancies. Among them, leiomyosarcoma is even rarer. According to the current international literature, only 10 cases have been reported. No domestic report. Our hospital met one case and the report is as follows.