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Nieman—Pick病为一种先性家族性脂类代谢障碍病,主要表现于网状内皮系统、神经系统等处有广泛的鞘磷脂(Sphingom-yelin)沉着。本病分别于1914年由Nieman和1922年由Pick首先描述。国内于1959年始有报告,我国称为神经网状内皮细胞病,至今例数未越20例,现报告一例。班×,女,1岁3个月。1980年1月17日因肤色苍白一年入院。病儿足月顺产第四胎,产后一般情况尚可,曾患“肺炎”,以后常有发热、咳嗽。
Nieman-Pick disease is a familial familial disorder of lipid metabolism that manifests itself mainly in the reticuloendothelial system and extensive sphingomyelin deposition in the nervous system. The disease was first described by Nieman in 1914 and Pick in 1922, respectively. Domestic reports began in 1959, China is called neural reticuloendothelial disease, the number of cases so far not more than 20 cases, a report is now reported. Class ×, female, 1 year old 3 months. January 17, 1980 pale due to hospitalization for one year. The sick child full-term follow-up of the fourth child, postpartum general situation is acceptable, had “pneumonia”, often after fever, cough.