家族性良性天疱疮(ｂｅｎｉｇｎｆａｍｉｌｉａｌｐｅｍｐｈｉｇｕｓ)又称Ｈａｉｌｅｙ-ｈａｉｌｅｙ病,是一种少见的不规则的常染色体遗传皮肤病。该病以皮肤易摩擦部位疱性病损为特征,口腔表现罕见。作者近来收治1例有口腔表现的患者,其口腔表现极易与白斑相混淆,现报告如下 Familial benign pemphigus (benignfamilialpemphigus), also known as Hailey-hailey disease, is a rare irregular autosomal genetic dermatosis. The disease is characterized by easy rubbing of the skin with blister lesions and rare oral manifestations. The author recently admitted to a patient with oral manifestations, the oral manifestations easily confused with the white spot, are as follows