先天性心脏病(以下简称先心病)的发病率约占出生婴儿的6～8‰。其中严重畸形如不早期治疗,多在1岁以内夭折或并发肺血管梗阻性病变而失去手术时机。至今已报告有12种左右先心病可并发肺血管病变。婴儿期常见的有大型室隔缺损、动脉导管未闭、完全性大动脉转位、完全性肺静脉异位引流、房室管畸形以及少见的总动脉干和右室双出口畸形,其中完全性大动脉转位伴室隔缺损发生肺血管病变尤早且重。房隔缺损在婴儿较少伴发肺高 The incidence of congenital heart disease (hereinafter referred to as congenital heart disease) accounts for about 6 to 8% of infants born. Severe deformities, such as if not early treatment, and more than 1 year old or died of pulmonary vascular obstruction and loss of operation timing. Has so far reported about 12 kinds of congenital heart disease may be complicated by pulmonary vascular disease. Common infants are large ventricular defects, patent ductus arteriosus, complete aortic transposition, complete anomalous pulmonary venous drainage, atrioventricular canal deformity and common trunk and right ventricle double outlet deformity, in which the complete aortic transfer Pulmonary venous disease with parotid septal defect especially early and heavy. Atrial septal defect in infants less associated with high lung