目的 :探讨腓骨肌萎缩征的病程规律及足部畸形手术时机和方式。方法 :临床治疗、随诊两家系 6例 ,手术治疗 4例 8足 ,随访时间 4 .5个月～ 2 0年。结果 :病程早期软组织手术 3例 6足 ,5足畸形复发 ,2例 (次 ) 4足晚期骨性手术尚满意。结论 :足部畸形进展并非均速进行 ,呈现缓—快—缓—停的规律 ,手术时间尽量推迟 ,最好选在快速进展期之后进行 ,争取一次手术解决问题。 Objective: To investigate the course of the disease and the timing and method of foot deformity. Methods: Clinical treatment, follow-up of two families in 6 cases, surgical treatment of 4 cases 8 feet, follow-up time of 4.5 months to 20 years. Results: The early course of soft tissue surgery in 3 cases 6 feet, 5 feet deformity recurrence, 2 cases (times) 4 feet late bony surgery is still satisfied. Conclusion: The progress of foot deformity is not uniform, showing the law of slow - fast - slow - stop, the operation time as far as possible delayed, the best choice after the rapid progress, and strive for a surgical solution to the problem.