报道1例少见的由孕母患肾上腺男性化肿瘤,引起阴茎尿道女性假两性畸形,术后经病理确诊。作者结合文献进行了讨论,当有男性化表现的母亲所生隐睾的男婴,应通过作性染色体验证.以便排除假两性畸形;对不能解释的女性假两性畸形,应探查其母亲是否患有男性化肿瘤的可能. Reported a rare case of male infertility masculine adrenal tumors, causing penile urethra female pseudohermaphroditism, postoperative pathological diagnosis. The authors have discussed the literature, when masculine performance of the mother of cryptorchidism caused by male testes should be verified by sex chromosome in order to rule out bisexual deformity; female unexplained bisexual deformity, should explore whether their mothers suffering from There is the possibility of masculine tumors.