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该综合征主要表现为多发性周围神经病、脏器肿大、内分泌紊乱、M-蛋白、皮肤改变,以及低热、多汗、杵状指、血沉快、γ-球蛋白增高、骨髓浆细胞增加,伴或不伴骨硬化性兼融骨性骨髓瘤等。它是一种与浆细胞有关的自家免疫异常性多系统损害综合征。 本文报道我院1990～1993年间收治的6例Crow-Fukase(又称POEMS)综合征患者,并收集1987～1993年国内20篇报道中资料较完整的38例与国外同类资料进行比较。目的是提高对本综合征的认识,及时治疗,以期取
The syndrome is mainly manifested as multiple peripheral neuropathy, organ enlargement, endocrine disorders, M-protein, skin changes, and fever, hyperhidrosis, clubbing, erythrocyte sedimentation rate, increased gamma globulin, increased bone marrow plasma cells, With or without osteopetrosis and metabonomia and so on. It is a plasma cell-related autoimmune multiple system damage syndrome. This article reports 6 cases of Crow-Fukase (POEMS) syndrome treated in our hospital from 1990 to 1993. We collected 38 cases of more complete data from 20 domestic reports from 1987 to 1993 and compared with similar foreign data. The purpose is to raise awareness of the syndrome, timely treatment, in order to obtain