比较分析 10例Ⅳa型先天性胆管扩张症与同期收治的Ⅰ型先天性胆管扩张症的临床症状、生化检查和胆汁淀粉酶、术后疗效等。对Ⅳa型先天性胆管扩张症的临床表现、可能的病因及手术方式等进行讨论。认为Ⅳa型先天性胆管扩张症也是此病的常见类型 ,其临床表现与Ⅰ型相同 ,无特殊性 ,其病因与胰胆管连接异常等先天性因素有关 ,目前仍以肝外囊肿切除术为首选术式 Comparative analysis of 10 cases of type Ⅳ a congenital bile duct dilatation and congenital type Ⅰ congenital bile duct dilatation clinical symptoms, biochemical tests and bile amylase, postoperative efficacy. Ⅳa type of congenital bile duct dilatation clinical manifestations, possible causes and surgical methods were discussed. That type Ⅳ a congenital bile duct dilatation is also a common type of disease, its clinical manifestations and type Ⅰ the same, no particular, the etiology and pancreaticobiliary abnormalities such as congenital factors, is still still the extrahepatic cyst excision as the preferred Surgery