目的:探讨鼻腔呼吸道上皮腺瘤样错构瘤的临床特点和诊治方法。方法:对14例鼻腔呼吸道上皮腺瘤样错构瘤患者临床资料进行回顾性分析和总结。所有患者均于全身麻醉下鼻内镜下行鼻腔肿物切除术、鼻窦开放术。结果:14例患者中,所有患者均为双侧病变,于嗅裂区可见广基弥漫性生长的息肉样新生物,呈粉红色或粉白色,大部分肿物质韧,触之不易出血,10例患者中鼻道及总鼻道同时可见鼻息肉;鼻窦CT检查均提示双侧鼻腔(嗅裂区)可见软组织密度影,伴不同鼻窦内黏膜增厚,密度增高,均无骨质破坏。对患者术后定期随访,均恢复良好,未见复发。结论:鼻腔呼吸道上皮腺瘤样错构瘤虽罕见,但其症状、体征及影像学检查无诊断性的特异表现,容易误诊和漏诊,只有增加对该病的认识和了解,才能提高诊断率。 Objective: To investigate the clinical features, diagnosis and treatment of nasal airway epithelial adenomatous hamartoma. Methods: The clinical data of 14 patients with nasal respiratory adenoma-like hamartoma were retrospectively analyzed and summarized. All patients underwent endoscopic nasal resection and sinus surgery under general anesthesia. Results: All 14 patients were bilateral lesions. In the olfactory fissure zone, there were diffuse polypoid polygons growing in pink or pinkish white color. Most of the tumors were difficult to hemorrhage and ten Cases of nasal and nasal polyps can be seen at the same time the nose; sinus CT examination showed bilateral nasal (olfactory fissure) soft tissue density can be seen with different sinus mucosa thickening, increased density, no bone destruction. Regular follow-up of patients after surgery, were recovered well, no recurrence. CONCLUSIONS: Nasal airway epithelial adenomatous hamartomas are rare, but their symptoms, signs and imaging findings are non-diagnostic and specific. They are easy to be misdiagnosed and missed. Only by increasing understanding and understanding of the disease, can the diagnostic rate be raised.