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血管母细胞瘤或Lindau 肿瘤属于罕见肿瘤。据统计占全部脑瘤的1—2%。最常见于后颅凹,约占该部肿瘤7.3—12%,亦见之椎管等。约3/4病例肿瘤主要为囊性变伴有小的壁在性实体结节,此外主要为实体性肿瘤伴有中央坏死或小囊形成。囊性变与周围组织分界清晰,而肿瘤实体部分则可侵及邻近脑组织,但其组织学均相同。此瘤之特殊伴随征象为红细胞增多症,后者见于5—31%病例。亦常常出现视网膜血管瘤(V—Hippel-Lin-dau 综合征)。
Hemangioblastomas or Lindau tumors are rare tumors. According to statistics, accounting for 1-2% of all brain tumors. The most common in the posterior fossa, about the Department of cancer 7.3-12%, also see the spinal canal. About 3/4 cases of cancer mainly cystic degeneration with small walls in the solid nodules, in addition to the main solid tumor with central necrosis or vesicle formation. Cystic degeneration and the surrounding tissue clear boundaries, while the solid part of the tumor can invade adjacent brain tissue, but its histology are the same. The specific signs of this tumor are polycythemia, the latter seen in 5-31% of cases. Retinal hemangiomas (V-Hippel-Lin-dau syndrome) are also frequently present.