目的　总结小儿共济失调的病因、临床特点及早期干预的疗效。方法　检查血清铜蓝蛋白、2 4h尿铜、肝肾功能、头颅MRI、脑电图 ,及早发现引起共济失调的病因 ,针对病因给予干预。结果　经早期干预 ,1～3周后 14例基本治愈 ,2例好转 ,3例行手术治疗 ,总有效率达 89.5 %。结论　小儿共济失调可由多种病因引起 ,临床特点以步态不稳、口齿不清起病 ;早期干预直接影响到患儿的预后及生存质量。 Objective To summarize the etiology and clinical characteristics of pediatric ataxia and the curative effect of early intervention. Methods Serum ceruloplasmin, 24 h urinary copper, liver and kidney function, cranial MRI and electroencephalogram (EEG) were examined. The cause of ataxia was detected and the cause of ataxia was given. Results After early intervention, 14 cases were basically cured after 1 to 3 weeks, 2 cases improved and 3 cases operated surgically. The total effective rate was 89.5%. Conclusions Pediatric ataxia can be caused by a variety of causes. The clinical features include unstable gait and slurred speech. Early intervention directly affects the prognosis and quality of life of children.