肾血管平滑肌脂肪瘤(AML)是一种少见肾脏良性间叶性肿瘤,由三种成份构成,即厚壁血管、平滑肌及脂肪按不同的比例混合而成。通常平滑肌成份较多,脂肪最少,临床上肿物大小不同,可单发或双侧,也可与肾癌伴发。因其平滑肌成份多有异型,且肿瘤可侵及肾周脂肪,累及淋巴结,可能被误诊 Renal angiomyolipoma (AML) is a rare renal benign mesenchymal tumor composed of three components, namely, thick-walled blood vessels, smooth muscle and fat mixed in different proportions. Usually more smooth muscle components, the least fat, clinically different size of the tumor can be single or bilateral, but also with renal cell carcinoma. Because of its smooth muscle composition and more shaped, and the tumor can invade the perirenal fat, involving the lymph nodes, may be misdiagnosed