享丁顿舞蹈病又称遣传性舞蹈病、慢性进行性舞蹈病。本病病因不明，主要是弥漫性脑的变化与脑重量减轻，尤以大脑皮层及尾状核明显萎缩和侧脑室扩大为病理特征。我们对一个家系进行了实地调查，发现在 6代人中有本病患者 15例，是典型的常染色体显性遗传，报告如下。1 病例资料 Also known as Dundun chorea sent choreography, chronic progressive chorea. The etiology of this disease is unknown, mainly diffuse brain changes and brain weight loss, especially in the cerebral cortex and caudate nucleus significantly shrinking and enlargement of the lateral ventricle for the pathological features. We conducted a field survey of a pedigree and found that there are 15 patients with this disease in 6 generations, is a typical autosomal dominant inheritance, the report is as follows. 1 case information