RIEGER氏综合征为一中胚层发育不全的遗传性疾病。通常表现为角膜、前房角、虹膜的中胚层发育不全,牙齿,上颌骨发育不良,脐周皮肤残留或发育不全等,并可伴发青光眼。本病较为罕见,现将我院所见一例报告如下: 李××,男,8岁,1984年12月29日入院。主诉 RIEGER’s syndrome is a hereditary disease of mesodermal hypoplasia. Usually manifested as cornea, anterior chamber angle, the iris mesoderm hypoplasia, teeth, maxillary dysplasia, umbilical skin residue or hypoplasia, and may be associated with glaucoma. The disease is relatively rare, now see a case of our hospital as follows: Lee × ×, male, 8 years old, December 29, 1984 admission. Chief complaint