原发性中枢神经系统血管炎 (primaryangiitisofthecen tralnervoussystem ,PACNS)是一种只局限侵犯中枢神经系统血管 ,而不累及其他系统的炎症性疾病。患者常仅有神经系统症状的临床表现 ,但神经定位又不很明确 ,脑脊液检查、脑CT及MRI均不能明确诊断 ,给诊断和治疗带来很大困? Primary central nervous system vasculitis (PACNS) is an inflammatory disease that limits violations of the central nervous system blood vessels without involvement of other systems. Patients often only the clinical manifestations of neurological symptoms, but the neurological location is not very clear, cerebrospinal fluid examination, brain CT and MRI can not be a clear diagnosis, diagnosis and treatment to bring great difficulties?