系统性红斑狼疮患儿常出现多脏器受累表现,其中肾脏是最常见的受累器官,但肾脏远曲小管功能受累者不多见。现将本例报告如下。 男,12岁。发热40天,伴面颊部红色皮疹,日晒加重,病后尿量增多,每日尿量2500～4000ml,尤以夜尿为多。病后第10日惊厥1次,为全身性发作,持续3分钟。惊厥前体温39℃。纳差,乏力,脱发,不伴关节痛,无咳嗽及胸痛,无多饮现象。病后曾先后应用红霉素,安渼汀,先锋治疗40天未见效。既往史及家庭 Multiple organ manifestations often occur in children with systemic lupus erythematosus, with the kidneys being the most common organ involved, but those with distal tubule involvement are rare. This case report is as follows. Male, 12 years old. Fever 40 days, accompanied by red rash cheeks, sun exposure, increased urine output after illness, daily urine output 2500 ~ 4000ml, especially nocturia. Convulsions on the 10th day after illness 1, for the systemic attack, sustained 3 minutes. Pre-convulsive temperature 39 ℃. Anorexia, fatigue, hair loss, without joint pain, no cough and chest pain, no drinking phenomenon. After the disease has been the application of erythromycin, An Ting Ting, Pioneer treatment for 40 days without results. Past history and family