肌萎缩侧索硬化(ALS)是一种进行性发展、上下运动神经元同时受累的神经系统变性病。根据临床和电生理检查所显示的病变累及范围,可以将ALS分为不同的诊断级别:临床确诊ALS、临床拟诊ALS、实验室支持-临床拟诊ALS以及可能的ALS。在ALS诊断过程中,肌电图具有重要的辅助作用。影像学和实验室检查有助于ALS和其他累及上下运动神经的疾病进行鉴别。 Amyotrophic lateral sclerosis (ALS) is a progressive degenerative disease of the nervous system that involves both upper and lower motor neurons. Based on the range of lesions shown by clinical and electrophysiological examinations, ALS can be divided into different diagnostic levels: clinically diagnosed ALS, clinically diagnosed ALS, laboratory support - clinically diagnosed ALS, and possibly ALS. Electromyography plays an important supporting role in the diagnosis of ALS. Imaging and laboratory tests help to identify ALS and other diseases involving the upper and lower motor nerve.