论文部分内容阅读
多囊肾病分为成人型与儿童型。前者多见,平均500例尸检中有1例,占终末期肾衰竭的5～7%。并发多囊肝约占30%。迄1983年底,国内共报道成人型多囊肾病218例,其中并发多囊肝者56例,占25.68%。我们报道一家族有4例患多囊肾病合并多囊肝。先证者Ⅲ_3,仇某,男,54岁。间歇性肉眼血尿32年。因周身奇痒,胃纳锐减,鼻衄50多天,昏睡1天入院。1972年血压高达240/120,伴轻度蛋白尿,曾误诊为慢性肾炎、肾性高血压。1980年又诊为氮质血症。
Polycystic kidney disease is divided into adult and children. The former more common, an average of 500 cases of autopsy in 1 cases, accounting for 5 to 7% of end-stage renal failure. Polycystic liver disease accounts for about 30%. As of the end of 1983, a total of 218 cases of adult polycystic kidney disease were reported in our country, including 56 cases of polycystic liver disease (25.68%). We report a family of 4 patients with polycystic kidney disease complicated with polycystic liver disease. Proof Ⅲ_3, Qiu a, male, 54 years old. Intermittent gross hematuria 32 years. Due to the whole body itching, appetite reduction, epistaxis more than 50 days, lethargy 1 day admission. Blood pressure in 1972 up to 240/120, with mild proteinuria, has been misdiagnosed as chronic nephritis, renal hypertension. In 1980 and diagnosed as azotemia.