先天性外科畸形是指胎儿期或出生时存在一种结构上缺陷 ,其可由单独一种畸形或多种畸形构成一种综合征。据统计 ,较大的先天性畸形发生率在 1/ 5 0 0～ 1/ 10 0 0。甚至有个别报告新生儿畸形发生率似乎更高 ,如 :Herper(1988)报告约 1%～ 3%新生儿有较明确畸形且影响到生活质量 Congenital surgical deformity refers to the fetal or birth of a structural defect, which may be a single deformity or multiple deformities constitute a syndrome. According to statistics, the incidence of larger congenital malformations in 1/500 ~ 1/100. It is even reported that there appears to be a higher incidence of neonatal deformities in individual cases. For example, Herper (1988) reported that about 1% to 3% of newborns have a more definite deformity and affect the quality of life