窦组织细胞增生症伴巨大淋巴结病(Sinushistiocytosis with massive lymphadenopathy,SHML)是一种罕见的疾病,慢性经过,为假淋巴瘤样良性病变,多发生于儿童和年青人,常为双侧无痛性颈淋巴结肿大,可伴其它部位的淋巴结病变,伴一处或多处结外受累者占28%,如眼眶、眼睑、腮腺、鼻副窦 Sinusitis and Cystic Lymphopathy (Sinusitis and Cytomegalomatosis with massive lymphadenopathy, SHML) is a rare disease that is chronic, pseudolipoma-like benign disease, and occurs mostly in children and young people, often bilateral painless Cervical lymph nodes, may be associated with other parts of the lymph node lesions, with one or more extra-28% involvement, such as the orbit, eyelid, parotid gland, nasal sinus