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目的 探讨儿童系统性红斑狼疮血液学改变的特征。方法 检测 6 9例红斑狼疮患儿的血常规、凝血、纤溶功能指标及药物作用前后的变化并予以分析。结果 男性与女性儿童重度贫血及全血细胞减少的发生率有显著性差异 (P <0 .0 5 ) ,30例患儿中有 5例PT ,KPTT延长、FIB降低 ;2 1例仅KPTT延长 ,经治疗后 17例恢复正常 ;10例FIB增多、尿FDP增多 ;2 1例D Dimer阳性。结论 儿童红斑狼疮血液系统异常与临床情况密切相关。
Objective To investigate the characteristics of hematological changes in children with systemic lupus erythematosus. Methods Sixty-nine children with lupus erythematosus were enrolled in the study. The blood coagulation and fibrinolytic function were measured and analyzed before and after treatment. Results There was a significant difference in incidence of severe anemia and pancytopenia between male and female children (P <0.05). PTT and KPTT prolonged and FIB decreased in 5 of 30 children. Only KPTT prolonged in 21 cases, After treatment, 17 cases returned to normal; 10 cases of FIB increased urinary FDP increased; 21 cases of D Dimer positive. Conclusion The abnormal blood system in children with lupus erythematosus is closely related to the clinical situation.