中枢神经系统血管外膜细胞瘤(HPC)极为罕见,其发生率占所有中枢神经系统肿瘤不足1%,共计100例病例被报道[1]。一般发生在大脑凸面、小脑幕、硬脑膜静脉窦及颅底等部位,也可发生在椎管内。在WHO 1993年分期中血管外膜细胞瘤被列为中枢神经系统肿瘤的一组特殊类别,而在1997年和2 Central nervous system vascular adventitial tumor (HPC) is extremely rare, its incidence of less than 1% of all central nervous system tumors, a total of 100 cases were reported [1]. Generally occurs in the convex surface of the cerebellum, cerebellar curtain, dura and sinus skull base and other parts, can also occur in the spinal canal. In the WHO 1993 staging of vascular adventitial tumor was classified as a special category of central nervous system tumors, and in 1997 and 2