成人原发肾病综合征(NS)伴范可尼综合征(FS)临床上比较少见。本文报告6例成人NS伴FS患者,对其临床表现、肾小管功能检查结果及肾病理表现作了介绍,并对其可能的发病机理进行了讨论。 Adult primary nephrotic syndrome (NS) with Fanconi’s syndrome (FS) is relatively rare clinical. This article reports 6 adult patients with NS with FS, its clinical manifestations, renal tubular function test results and renal pathological findings were introduced, and its possible pathogenesis were discussed.