间质性肺疾病(Interstitia1 Lung Diseasc简称ILD)是一组以肺间质病变为主的异型疾病.是以肺泡壁为主要病变的一组疾病群。它以弥漫性肺泡炎并进展为肺间质纤维化为主要病理特征,以缓慢加剧的进行性呼吸困难为其主要临床表现,以大部分肺野布满粟粒状、网线状或蜂窝状影为其主要x线特点。这是一组病因不同、临床特征各异又有许多共同之处,病理基础和病理生理都比较复杂的疾病,临床诊断和 Interstitial Lung Disease (Interstitial Lung Symptoms, ILD) is a group of dysplasia with interstitial lung disease as the main group of diseases with alveolar wall as the main lesion. It diffuse alveolitis and progress to the main pathological features of interstitial fibrosis, with slowly progressive progressive dyspnea as its main clinical manifestations, most of the lung fields covered with miliary, mesh or honeycomb-like Its main x-ray features. This is a group of different etiology, different clinical features and many have in common, the pathological basis and pathophysiology are more complex diseases, clinical diagnosis and