Ｂｕｄｄ Ｃｈｉａｒｉ综合征的发病率为 2 4人 /1 0 0万人 ,是一种发病率较低的疾病。此综合征是结节性病变 ,尤其以合并于原发性肝癌而引起人们的关注。本病是在 1 845年由英国医师ＧｅｏｒｇｅＢｕｄｄ首次在临床上开始认识 ,直到 1 899年由德国病理学者ＨａｎｓＣｈｉａｒ The incidence of Budd Chiari syndrome is 24 people / 10 million people and is a disease with a low incidence. This syndrome is a nodular disease, especially in patients with primary liver cancer caused by the attention. The disease was first realized in 1845 by the British physician GeorgeBudd in clinical practice until 1899 by the German pathologist HansChiar