纯词聋是临床上较为罕见的一种神经异常症象。现将我们所见1例患者报告如下。 患者男,28岁,右利手。因“语言理解障碍,表达障碍12年”于1995年6月23日收入院。入院诊断“脑炎后遗症”。住院查体:意识清醒,表情自如,神经系统检查未见异常,感觉运动功能正常,ADL自理;中国康复研究中心失语症检查;自发言语语量少、流畅,伴错语、杂乱语,听理解严重障碍,名词正答率仅为30％,动词及句子理解均为0。复述不能,听写不能,说、出声读相对较好,平均达70％～80％。阅读、抄写、描写及计算能力基本正常,正答率均在90％～100％。10种常用社会环境音辨别(包括鼓声、雷声、牛叫声、羊叫声、火车声、汽车声、铃铛声、哭泣声、笑声、咳嗽声)正答率50％。纯音听力检查及听觉诱发电位检查双侧均正常;脑部MRI表现:全脑皮质萎缩,尤以双侧颞、顶叶为甚,脑沟、回加深,并可见第5、6脑室。 本病例病程长达12年之久,发病于“急性暴发 Pure word deafness is a rare clinical evidence of neurological abnormalities. Now we see a patient reported below. Male patient, 28 years old, right hand. Because of “language understanding obstacle, expression obstacle 12 years” on June 23, 1995 income courtyard. Admission diagnosis “Encephalitis sequelae.” Inpatient physical examination: conscious, facial expression, nervous system examination showed no abnormality, sensory motor function is normal, ADL take care of themselves; Chinese Research Center of Aphasia examination; less verbal, smooth, with the wrong language, chaotic language, listening comprehension Serious obstacles, the rate of correctness of nouns is only 30%, verbs and sentences are all 0. Can not repeat, can not dictate, say, speak out relatively good, an average of 70% to 80%. Read, copy, description and calculation ability is normal, the rate is 90% to 100%. 10 kinds of commonly used social environment sound discrimination (including drum sound, thunder, barking, sheep sounds, train sound, car sound, bells sound, crying sound, laughter, cough sound) is the rate of 50%. Pure tone audiometry and auditory evoked potentials were normal on both sides; brain MRI manifestations: cortical atrophy, especially bilateral temporal, parietal lobe, sulci, back to deepen, and can be seen in the fifth ventricle. The duration of this case up to 12 years, the incidence of "acute outbreak